C9orf72 GGGGCC Repeat Expansion

Purpose

To detect expansion of a hexanucleotide GGGGCC repeat in the Chromosome 9 open reading frame 72 (C9ORF72) gene.

The expansion of a hexanucleotide GGGGCC repeat in C9ORF72 is the most common genetic cause of amyotrophic lateral sclerosis (ALS) and frontotemporal dementia (FTD). This test detects the C9ORF72 expansion mutation in approximately 37% of familial ALS and 25% of familial FTD patients.

CPT Codes

81479

Methodology

Capillary Electrophoresis

Turnaround Time

14 days

Specimen

Blood

Forms